摘要
门静脉海绵状瘤胆管病(portal cavernoma cholangiopathy,PCC)为门静脉海绵状瘤继发的胆管形态结构异常,多见于肝外门静脉阻塞(extrahepatic portal venous obstruction,EHPVO)患者,其发病机制尚不完全明确,可能与胆道受压、缺血、炎症等有关。磁共振胰胆管造影是其首选检查方法,有症状者可给予内镜治疗、外科手术或介入治疗,但无统一的治疗标准。本文旨在对PCC的发病机制、临床表现、诊断、治疗方式等研究进展作一综述,以期提高临床医师对该病的认识。
Portal cavernoma cholangiopathy(PCC)refers to cholangiographic abnormalities secondary to portal cavernoma,which often occurs in patients with extrahepatic portal venous obstruction(EHPVD).Its pathogenesis is unclear and may be related to bile duct compression,ischemia and inflammation.Magnetic resonance cholangiopancreatography is the first choice of examination.Symptomatic patients can be given to endoscopic treatment,surgery or interventional treatment,however,there is no consistent standard about treatment.This review aimed to summarize the research progress of pathogenesis,clinical manifestations,diagnosis and treatment methods about PCC for improving the clinicians′perception.
作者
邱秋
刘凯军
李国均
QIU Qiu;LIU Kaijun;LI Guojun(Department of Gastroenterology,People′s Hospital of Chongqing Hechuan,Chongqing 401520;Department of Gastroenterology,Daping Hospital,Army Medical University;Department of Hematology,People′s Hospital of Chongqing Hechuan,China)
出处
《胃肠病学和肝病学杂志》
CAS
2023年第1期114-117,共4页
Chinese Journal of Gastroenterology and Hepatology
关键词
门静脉海绵状瘤胆管病
发病机制
诊断
治疗
Portal cavernoma cholangiopathy
Pathogenesis
Diagnosis
Treatment
