摘要
目的探讨小儿蛋白丢失性肠病的临床诊疗思路。方法通过对2例蛋白丢失性肠病患儿的临床表现、诊治经过、随访观察、治疗反应,并结合文献复习进行综合分析。结果两患儿均系婴儿,临床表现主要为腹泻、低蛋白血症,可伴随其他系统相关症状,行消化内镜+病理活检或核素检查诊断为蛋白丢失性肠病、小肠淋巴管扩张症,给予水解蛋白配方奶粉喂养等治疗后症状缓解。结论临床上对于低蛋白血症的患儿,在除外肝肾疾病和营养不良的基础上,应尽早进行淋巴管扩张症乃至蛋白丢失性肠病的排查,以提高疾病的诊治率及患儿的生存质量。
Objective To explore the clinical diagnostic and therapeutic train of thought of children＇s protein losing enteropathy （PLE）. Methods The information about clinical manifestation, diagnostic course, therapeutic action of two patients with PLE were collected and analyzed, and the literatures were reviewed. Results Two patients were also infants, with clinical manifestation including diarrhea and hypoalbuminemia, some followed with correlated phenomena in other systems, and diag nosed as PLE or intestinal lymphangiectasia through digestive endoscopic biopsy and radiographic imaging examination. Their symptoms relieved after giving milk protein hydrolysates and others. Conclusion It＇s necessary to screen intestinal lymphangiectasia even PLE as soon as the children with hypoalbuminemia have excluded liver＇s disease, renal involvement or malnutrition, so as to improve the cure rate and living quality.
出处
《福建医药杂志》
CAS
2016年第3期21-24,共4页
Fujian Medical Journal
关键词
蛋白丢失性肠病
低蛋白血症
小肠淋巴管扩张
诊治
小儿
protein losing enteropathy
hypoalbuminemia
intestinal lymphangiectasia
diagnosis and therapy
children
