摘要
目的 探讨CT与MRI在诊断Sturge Weber综合征中的价值。方法 收集Sturge Weber综合征的病例共 9例。所有患儿均行常规CT扫描和MRI检查 ,其中 2例同时行MRI增强扫描。结果 ①CT表现 :6例一侧脑叶受累 ;2例双侧额顶叶均受累 ;1例CT未见异常。其中 5例脑叶呈中重度萎缩 ;8例皮层内出现脑回状钙化 ;3例一侧受累脑叶灰白质分界不清 ;2例合并一侧脉络丛扩大 ;1例合并有深静脉血管团出现。②MRI表现 :9例MRI中 5例一侧脑叶受累 ;4例双侧额顶枕叶均受累。所有患儿均有不同程度的脑萎缩 ,其中轻度者 4例 ,中度者 3例 ,重度者2例。仅有 2例在萎缩的皮层下出现钙化 ;8例受累脑叶灰白质分界不清 ;5例一侧脑室内脉络丛呈囊状扩大 ;3例一侧颅板板障增厚 ;4例于侧脑室旁、室管膜下区出现粗大的静脉团。 2例增强扫描后 ,受累侧皮层出现脑回状强化。结论 MRI与CT的综合分析 。
Objective To compare the efficacy of CT and MRI in the diagnosis of Sturge Weber syndrome in nine cases. Methods Nine children suffered from Sturge Weber syndrome were included in this study. Routine CT and MR examination were performed in all nine cases. In 2 cases, a contrast enhanced T1 weighted SE sequence was carried out. Results ① CT findings: CT showed abnormal cerebral involvement which were bilateral in two cases, ipsilateral in six, except in one case with normal appearance. Among them, cerebral lobar atrophy was moderate and marked in five cases. In 8 of all 9 cases, cerebral calcifications were demonstrated within cortical areas. The choroid plexus was enlarged with respect to the contralateral plexus in only two patients. Enlarged vessel was present in deep cerebral region in one case. And the interfaces between gray matter and white matter were blur in three cases. ② MRI findings: The cerebral lobar involvement showed bilateral in four cases, ipsilateral in five. Atrophy was slight in four cases; moderate in three; marked in two. Calcification was demonstrated in only two cases while no cortical calcification was seen in seven other cases. The choroid plexus was enlarged with respect to the contralateral plexus in five patients. The interfaces between gray matter and white matter were blur in eight cases. Moreover, enlarged vessels were present in the subependymal and periventricular regions in four cases. The thickness of cranial diploe was present in three cases. After contrast administration in two cases, enhancement was noted within involved cortical areas. Conclusion MRI ,combined with CT plays an important role in the diagnosis of Sturge Weber syndrome.
出处
《中国医学影像技术》
CSCD
2001年第1期31-33,共3页
Chinese Journal of Medical Imaging Technology
