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无脾综合征患者体肺静脉回流特点分析 被引量:5

Characteristics of vena cava connection in patients with asplenia
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摘要 目的探讨无脾综合征患者体、肺静脉回流特点,为超声诊断该类疾病提供依据。方法 2009年10月至2014年2月在阜外心血管病医院就诊,经作者行超声心动图检测的无脾综合征患者49例,分析患者体、肺静脉回流特点及各类常见畸形引流的发生频次。结果 49例患者超声心动图检测显示双上腔静脉30例(61.2%),均为右上腔静脉入右心房(或单心房右侧),左上腔静脉入左心房(或单心房左侧);肝静脉全部汇入下腔静脉26例(53.2%);直接汇入左心房(或单心房左侧)1例(2.1%);直接汇入右心房(或单心房右侧)3例(6.3%);分别汇入两侧心房5例(10.2%);汇入单心房中部1例(2.1%);部分汇入下腔静脉,部分直接汇入心房13例(27.7%)。下腔静脉直接汇入左心房(或单心房左侧)18例(36.2%);直接汇入右心房(或单心房右侧)25例(51.0%);引流入单心房中部1例(2.0%)。部分肺静脉异位引流8例(16.3%),均为心上型;完全性肺静脉异位引流20例(40.2%),其中心上型11例(55%);心内型7例(35%),心下型1例(5%);混合型1例(5%)。结论无脾综合征患者多伴有体静脉与肺静脉异位引流。 Objective To investigate the characteristics of vena cava connection in patients with asplenia syndrome diagnosed by ultrasound. Methods From October 2009 to February 2014, 49 patients with asplenia syndrome diagnosed in Fuwai Hospital by ultrasound were included in this study. The characteristics and percentage of varied types of anomalous connection of vena cava and pulmonary vena were analyzed. Results Thirty patients(61.2%) had bilateral superior vena cavies. In these cases, right vena cava was drainage into right atrium(or the right side of the single atrium), while left superior vena cava into left atrium(or the left side of the single atrium). For hepatic vein, drainage into inferior vena cava were found in 25 patients(53.2%), into left atrium(or the left single of the single atrium) in 1 patient(2.1%), into right atrium(or the right side of the single atrium) in 3 patients(6.3%), into both right and left atrium in 5 patients(10.2%) and into the middle of the single atrium in 1 patient(2.1%). For inferior vena cava, drainage into left atrium(or left side of the single atrium) were found in18 patients(36.2%), into right atrium(or right side of the single atrium) in 24 patients(51.1%) and into the middle of the single atrium in 1patient(2%). Total anomalous pulmonary venous drainage occurred in 20 patients(40.2%) and partially anomalous pulmonary venous drainage in 8 patients(16.3%). Conclusion Asplenia syndrome is frequently accompanied with anomalous vena cava and pulmonary venous drainage.
出处 《中华医学超声杂志(电子版)》 CSCD 2015年第2期160-164,共5页 Chinese Journal of Medical Ultrasound(Electronic Edition)
关键词 超声心动描记术 压力 肺静脉 Spleen Echocardiography,stress Pulmonary veins
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同被引文献45

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