摘要
目的研究先天性小耳畸形合并泌尿生殖系统先天畸形的发病率,分析两者的相关性。方法回顾性分析2015年1月至2019年12月3143例小耳畸形患者,通过肾脏超声或腹部CT检查,统计其中合并泌尿生殖系统畸形的病例,并对其畸形进行分类;对先天性小耳畸形合并泌尿生殖系统畸形患者的发病情况、患耳侧别与泌尿生殖系统畸形侧别之间的相关性等进行分析。结果在3143例小耳畸形患者中,163例伴有泌尿、生殖系统方面的畸形,包括单侧肾脏缺如、肾脏发育不全、肾脏积水、尿道下裂、睾丸发育异常等,总发病率为5.2%。数据分析显示,先天性小耳畸形伴发先天性泌尿生殖系统畸形的患者中,Ⅱ度小耳畸形的占比最高,肾积水、肾囊肿和睾丸发育异常的占比较高,且先天性小耳畸形的侧别与先天性泌尿系统畸形的侧别具有相关性。结论泌尿生殖系统畸形在先天性小耳畸形患者中比一般人群中发病率高,且两者大概率是同侧畸形,可通过体格检查、肾脏超声及腹部CT诊断。先天性小耳畸形患者的诊疗中应关注患者肾脏功能,以改善此类患者预后。
Objective To study the incidence of congenital urogenital malformations in patients with congenital microtia,and to analyze the correlation between the two diseases.Methods A retrospective analysis was performed on 3143 patients with microtia from January 2015 to December 2019,and the cases with genitourinary system malformations were counted and classified through renal ultrasound or abdominal CT examination.The incidence of congenital microtia combined with genitourinary system malformations and the side correlation between the affected ear and urogenital deformities were analyzed.Results Among 3143 patients with congenital microtia,163 cases were accompanied by congenital genitourinary system malformations,including unilateral kidney deficiency,renal hypoplasia,hydronephrosis,hypospadias,and testicular deformity,with a total incidence of 5.2%.Through data analysis,it can be seen that among the patients with congenital microtia accompanied by congenital genitourinary malformation,the proportion of second-degree microtia was the highest,and the proportion of hydronephrosis,renal cyst and testicular deformity was relatively high.What’s more,the side of congenital microtia was associated with the side of congenital genitourinary malformations.Conclusion In patients with congenital microtia,the incidence of genitourinary malformation is higher than in the general population,and they both are more likely to be ipsilateral.Such patients can be diagnosed through physical examination,renal ultrasound and abdominal CT,so as to focus on renal function in subsequent treatment to improve the prognosis of these patients.
作者
高德瑾
王冰清
刘暾
章庆国
GAO Dejin;WANG Bingqing;LIU Tun;ZHANG Qingguo(The Second Center of External Ear Reconstruction,Plastic Surgery Hospital,Chinese Academy of Medical Sciences&Peking Union Medical College,Beijing 100144,China)
出处
《组织工程与重建外科》
CAS
2023年第3期265-269,共5页
Journal of Tissue Engineering and Reconstructive Surgery
