摘要
致心律失常性心肌病是一种纤维脂肪组织替代心室心肌,以室性心律失常和心脏性猝死为主要表现的遗传性心肌疾病。既往称之为致心律失常性右心室心肌病/发育不良。现已明确,该类疾病并非局限于右心室,双心室受累甚或左心室单独受累亦可见。现就致心律失常性心肌病的分类、机制与治疗进行综述。
Arrhythmogenic cardiomyopathy is an inherited rare disease characterized by a progressive myocardial fibrofatty replacement.It is associated with ventricular arrhythmias and sudden cardiac death.In the classic description,it has been called arrhythmogenic right ventricular cardiomyopathy/dysplasia.With the continuous enrichment of clinical studies,it has been found that this kind of disease is not limited to the right ventricle,but also exists in cases of bilateral ventricular involvement or left ventricular involvement alone.This paper reviews the latest research progress of arrhythmogenic cardiomyopathy.
作者
林晶
吉庆伟
刘伶
LIN Jing;JI Qingwei;LIU Ling(Department of Cardiology,The People s Hospital of Guangxi Zhuang Autonomous Region,Nanning 530021,Guangxi,China)
出处
《心血管病学进展》
CAS
2020年第12期1247-1250,共4页
Advances in Cardiovascular Diseases
基金
国家自然科学基金面上项目(81770472)
国家自然科学基金(81760051)
广西科技基地和人才专项(桂科AD17129026)
广西重点研发计划(桂科AB17292078)
广西壮族自治区卫生和计划生育委员会自筹经费科研课题资助(Z2018702)。
