摘要
1例男性新生儿表现为先天性乳糜性腹水,由于持续性丢失乳糜,所以治疗困难且复杂。初期的治疗目的是减少淋巴液流失并期待其自愈。通常采用保守治疗(完全双亲喂养肠道休息或经肠道进食中链甘油三酯)就能达到此目的。
A male newborn presented with congenital chylous ascites, the treatment of which is difficult and complicated due to persistent loss of chyle. The primary therapeutic goal is to reduce the lymph flow and to allow the leakage to heal naturally. Usually, conservative management-enteric rest with total parental feeding or an enteral diet with medium-chain triglycerides-can achieve this. A new treatment option is the use of octeotride, a somatostatin analogue. Both therapies failed in our patient, and surgical ligation of the leaking lymphatic duct was successful. Conclusion: The success of the surgical treatment depends on localizing the leaking lymphatic duct. Lymphatic imaging with lym-phoscintigraphy and pre-operative administration of lipophil-ic dye can assist the surgeon.