摘要
目的:分析肺动脉闭锁合并双侧动脉导管分别供应双肺血患者的影像学特点及其发生率。方法:回顾82例复杂先天性心脏病合并肺动脉闭锁患者的造影资料,分析肺血来源、肺动脉发育情况及合并畸形。结果:82例肺动脉闭锁患者中确定双侧动脉导管4例,其中病例1及2为肺动脉闭锁合并室间隔缺损,病例3及4为肺动脉闭锁合并无脾综合症。本组患者中双侧动脉导管未闭的总发病率为4.9%,在亚组分析中合并室间隔缺损及合并无脾综合症的发生率分别为3.1%和33.3%。结论:双侧动脉导管在肺动脉闭锁患者中的发生率非常低,明确诊断需要行心导管造影。建议在肺动脉闭锁合并无脾综合症的患者中应将双侧动脉导管作为常见的肺动脉供血方式加以明确。
Objective： Pulmonary atresia and rloneorlfluent central pulmonary arteries with both distal pulmonary arteries connected to the ipsilateral ductus arteriosus （DA） is a rare pattern of blood supply to the lungs. The aim of this study was to establish prevalence and anatomical pattern of bilateral DA in patients featu- ring pulmonary atresia. Methods ： We reviewed cardiac catheterization of 82 consecutive patients with complex congenital heart disease featuring pulmonary atresia from June 2011 and December 2016. Results： Bilateral pa- tent DA were diagnosed in 4 of 82 patients. Cases 1 and 2 were pulmonary atresia with ventrieular septal defect, case 3 and 4 were single vent^icle, pulmonary atresia associated with asplenia syndrome. The prevalence of hi- lateral DA in patients with pulmonary atresia is approximately 4. 9% , the prevalence in subgroup with ventricu- lar septal defect and asplenia syndrome were 3. 1% and 33.3%. Conclusion： The prevalence of bilateral DA in patients pulmonary atresia is low, the diagnosis may be missed without appropriate angiograms. We recom- mended that bilateral DA should be considered as a possible source of pulmonary blood flow in patients of pul- monary atresia with asplenia syndrome.
出处
《心肺血管病杂志》
2017年第11期914-917,共4页
Journal of Cardiovascular and Pulmonary Diseases
关键词
肺动脉闭锁
双侧动脉导管
无脾综合症
Bilateral ductus arteriosus
Pulmonary atresia
Asplenia syndrome
