摘要
目的:探讨中枢神经系统表面铁沉积症(SSCNS)的病因、临床和影像学特点等。方法:报道1例确诊的SSCNS患者,并检索CNKI、万方、维普数据库,对确诊的23例SSCNS患者,进行症状、体征、实验室检查的分类统计。结果:SSCNS起病形式多样,多为共济失调、听力障碍及头痛等。SSCNS多具有典型的共济失调(22/23)、听力障碍(16/23)、脊髓病变(20/23)等三联征。磁共振均有明显改变。结论:SSCN病程多在数年以上,起病形式各异,暂时无有效的治疗方式。
Objective：To discuss the etiology, clinical and radiographic features of superficial siderosis of the central nervous system（SSCNS）. Methods： One case of the SSCNS was reported, and the database of the CNKI, WANFANG med online were searched. The presentation, signs, lab examination, diagnosis and probable etiology of the 26 confirmed cases were reviewed. Results： The first symptoms of the SSCNs were diverse,such as cerebellar ataxia, sensorineural deafness and headache. SSCNs were defined as a combination of cerebellar ataxia（22/23）, sensorineural deafness（16/23） and myelopathy（20/23）. Conclusion： SSCNs often take more than a few years and have different disease forms, have no effective treatment currently.
出处
《神经损伤与功能重建》
2016年第3期222-224,共3页
Neural Injury and Functional Reconstruction
关键词
含铁血黄素
脑脊髓表面
蛛网膜下腔出血
hemosiderin
surface of the cerebrospinal
subarachnoid hemorrhage
