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沙利度胺治疗遗传性出血性毛细血管扩张症一例并文献复习

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摘要 报道应用沙利度胺成功治疗遗传性出血性毛细血管扩张症(HHT)所致出血患者1例。HHT是血管发育异常的一种常染色体显性遗传性疾病,多有家族史,多以鼻出血首发,内脏出血以胃肠道最多见,临床上主要以对症及支持治疗为主。本例提示沙利度胺可能是一种减少HHT发生出血的有效药物治疗手段,但尚需更多研究进行客观评估。
出处 《中华全科医师杂志》 2015年第6期465-466,共2页 Chinese Journal of General Practitioners
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