摘要
噬血细胞综合征(HPS)又称噬血细胞性淋巴组织细胞增生症(HLH),分为原发性HLH和继发性HLH两大类。HLH临床表现多样,其诊断需符合HLH诊断标准。治疗首选依托泊苷、地塞米松和环孢素A。本文总结近年来HLH病因、发病机制、诊断及治疗等方面的研究进展。
Hemophagocytic syndrome（HPS）is also knowed as hemophagocytic lymphohistiocytosis（HLH）, which is classified to FHLH and SHLH. The clinical manifestations are various and the diagnosis should be accorded with the HLH diagnosis standard. VP-16,dexamethasone and cyclosporin A are the first choice of treatment.In this review,the recent progress on the etiology,pathogenesis,diagnosis and treatment strategies of HLH have been described.
出处
《中国医学创新》
CAS
2014年第24期149-151,共3页
Medical Innovation of China
基金
广西壮族自治区卫生厅自筹资金科研课题(Z2013421)
关键词
噬血细胞综合征
诊疗
研究进展
Hemophagocytic syndrome
Diagnosis and treatment
Research progress
