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囊性肺纤维化 被引量:4

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摘要 囊性肺纤维化是一种家族常染色体隐性遗传的先天性疾病,在北美洲白人中常见,其他人种则极少见。常累及胃肠道和呼吸道,极易发生呼吸道感染而引起气道梗阻及呼吸功能不全,多数病人仅能成活数年到十余年。本文对该病病因、发病机制、诊疗措施以及预后等方面的进展进行了综述。
出处 《罕少疾病杂志》 2002年第2期30-32,共3页 Journal of Rare and Uncommon Diseases
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