摘要
目的提高对肝脏血管周上皮样细胞肿瘤这一罕见的肝脏原发性肿瘤的诊疗水平。方法回顾了2012年3月到2014年12月期间我中心确诊的4例原发性肝脏血管周上皮样细胞肿瘤的病历资料,对原发性肝脏血管周上皮样细胞肿瘤的临床特点、影像学表现、病理特点、治疗及预后进行分析。结果肝脏血管周上皮样细胞肿瘤缺乏特征性临床表现,影像学检查易与肝细胞癌、肝血管瘤等常见肝脏肿瘤混淆而导致术前诊断错误。手术治疗是治疗肝脏血管周上皮样细胞肿瘤唯一有效方法,研究收纳的4例患者术后随访均无复发。结论肝脏血管周上皮样细胞肿瘤是一种罕见的肝脏原发性肿瘤,应提高对其的认识,提高诊断治疗水平。
Objective To improve the diagnosis and treatment of perivascular epithelioid cells tumor (PEComa),a rare type primary tumor in liver.Methods The clinical data of 4 cases with hepatic PEComa who received surgical treatment in our center from March 2012 to December 2014 were collected.The clinical manifestations,imaging features,diagnostic and therapeutic strategies, pathologic features,prognosis were analyzed.Results Hepatic PEComa has no specific clinical manifestations.Imaging features simi- lar to common liver tumor,eg.hepatocellular carcinoma or hepatic hemangioma,might result in wrong diagnosis.Surgical resection is the only curative therapy.No recurrence was observed during the follow-up.Conclusion Hepatic PEComa is a rare type of primary liver tumor.Diagnosis and treatment of hepatic PEComa must be intensified.
作者
鲁皓
张传永
戴新征
LU Hao;ZHANG Chuan-yong;DAI Xin-zheng Dai(Hepatobiliary Center of Jiangsu Province Hospital.300 Guangzhou Road,Nanjing 210029,China)
出处
《肝胆外科杂志》
2018年第6期419-422,共4页
Journal of Hepatobiliary Surgery
