摘要
目的 探讨儿童胫骨骨与纤维发育不良的诊断、治疗与预后。方法 在复习文献的基础上 ,对 1992年以来手术治疗和门诊观察的 10例儿童胫腓骨骨与纤维发育不良的临床表现、X线特征和手术治疗结果进行回顾性分析。结果 7例手术刮除后都出现术后复发 ,1次复发者 2例、2次复发者 4例 ,3次复发者 1例。结论 儿童胫骨骨与纤维发育不良是一种侵袭性瘤样病变。在发病年龄、X线及病理表现、临床过程等方面 ,与单发性长骨纤维发育不良均有明显的区别。儿童期手术治疗极易复发 ,因此 。
Objective To study the diagnosis and treatment of osteofibrous dysplasia (OD) of tibia and fibula in children.Methods On the basis of review of literature, retrospective analysis was made on clinical and radiographic features and results of operation in 10 cases of OD of the tibia and fibula between 1992 and 1997.Results There were 7 boys and 3 girls in the series with age averaging 7 years and 3 months. The mean length of follow-up period was 5 years and 7 months. In 4 cases, only tibia was involved and in 6 cases both ipsi-lateral tibia and fibula were affected. The complaint on presentation was localized hard swelling and pain of tibia in 4 cases, anterior arch was found in 3 cases. 3 cases were asymptomatic. Radiographic findings included one or several eccentric intra-cortex osteolytic lesions with marked expansion of the external cortex and the inner surface of cortex was marginated by a band of sclerosis, which encroached and narrowed the medullary canal. There was anterior arch in 3 cases. Relapse occurred in 7 patients after curettage. Of them, 2 patients had one episode of recurrence; 2 had four episodes, and 1 had three episodes.Conclusions OD of the tibia and fibula in children is an bone tumor of aggressive nature, which differs from fibrous dysplasia in age distribution, radiographic features, histology and clinical course. The surgical treatment should be performed until the patients are skeletally mature.
出处
《中华小儿外科杂志》
CSCD
北大核心
2001年第6期370-371,共2页
Chinese Journal of Pediatric Surgery
