摘要
目的:探讨肝豆状核变性并肝硬化的MR表现,以期早期诊断。方法:对20例明确诊断为肝豆状核变性伴肝硬化患者的MR的表现进行回顾性分析。结果:肝、脾增大者8例;3例表现为肝脏多发再生结节,体积萎缩,肝裂增宽;6例表现为再生结节形成,肝脏体积萎缩,肝裂增宽,同时门静脉增宽,脾脏增大;3例表现为再生结节形成,门静脉增宽、脾大同时合并食道下段及胃冠状静脉曲张。结论:肝豆状核变性伴肝硬化MR检出率为100%,其MR表现具有一定的特征性,是早期诊断无神经系统锥体外系症状的肝豆状核变性的重要证据。
Objective:To explore the MR manifestations of cirrhosis in hepatolenticular degeneration to early diagnosis of it.Methods:Retrospective analysis of the MR fnddings of 20 Indeed dagnosed cirrhosis in hepatolenticular degeneration.Results:8 cases of patients showed liver and spleen enlargement;3 cases showed multiple regenerative nodules in the liver,shrinking liver volume,liver crack widened;6 cases of patients showed multiple regenerative nodules in liver volume atrophy,liver crack widened,and the portal vein was widened,the spleen enlargement;3 cases of patients showed multiple regenerative nodules,portal hypertension with lower esophageal and gastric coronary varices.Conclusion:There is a certain characteristic of MR appearance of cirrhosis in hepatolenticular degeneration and it is the early diagnosis of extrapytamidal symptoms in the nervous system,liver degeneration of important evidence.
出处
《中国医学创新》
CAS
2012年第16期91-92,共2页
Medical Innovation of China
关键词
肝豆状核变性
肝纤维化
肝硬化
磁共振成像
Hepatolenticular degeneration
Liver fibrosis
Cirrhsis of the liver
Magnetic resonance imaging
