摘要
噬血细胞综合征属于组织细胞增生性疾病，特征为组织细胞异常增生并具有吞噬血细胞现象。本文报道的１０例病列中，７例发现与感染相关，１例与肿瘤相关，２例未发现相关疾病。用大剂量丙种球蛋白治疗６例病人１例获得痊愈，３例临床症状好转，２例无效死亡。病例资料分析提示：血清甘油三脂增高和纤维蛋白原降低可能是预后不良的指标。
Hemophagocytic syndrome (HPS) is one type of histiocytosis. It is characterized by exaggerated histiocytic proliferation and hemophagocytosis. There were 10 cases reported. 7 of10 cases was associated with infection, 1 cases was associated with malignancy, the associated disease has not been found in 2 cases. Among 6 cases who was treated with high-dose γ-globulin, 1 cases become recovery, clinical symptom become better in 3 cases, 2 cases whodid not respond to the treatment died. The clinical data suggested that hypertrigly ceridemiaand hypofibrinogenemia predict a bad prognosis.
出处
《中国小儿血液》
CAS
1999年第5期198-199,共2页
China Child Blood
