摘要
目的:探讨Dandy-Walker综合征(DWS)的临床及MRI表现特征。方法:对6例经MRI诊断为DWS进行回顾性分析。结果:MRI主要表现为小脑蚓部缺如,小脑半球部分发育不全伴分离、移位;第四脑室囊状扩大与后颅窝囊腔相通;后颅窝扩张伴有横窦、窦汇和小脑幕上移;常伴有幕上不同程度梗阻性脑积水及其他颅内畸形。结论:DWS的MRI表现具有特征性,MRI是诊断DWS的最理想的影像学方法。
Objective：To explore the clinic and MRI features of Dandy-Walker syndrome（DWS）.Methods：The MRI findings of DWS（n=6） confirmed by MRI scan were analyzed retrospectively.Results：The main MRI findings of DWS were observed as follows： absence of the cerebellar vermis or partial agenesis of the separative cerebellar hemispheres,cystic dialation of the fourth ventricle communicating with enlargement of posterior fossa cyst,enlargement of posterior fossa with upward displacement of lateral sinuses,sinus confluens and tentorium,and often accompanying with differential supratentorial hydrocephalus of obstruction and other intracranial malformations.Conclusion：There are characteristic MRI findings in the DWS and MRI scan is a valuable method for an early diagnosis of DWS.
出处
《医学影像学杂志》
2010年第2期156-158,共3页
Journal of Medical Imaging
