摘要
目的提高对少见疾病Kimura病的认识。方法分析广州医学院第一附属医院广州呼吸疾病研究所于2008年7月29日收治的1例Kimura病伴支气管扩张患者的临床和病理资料,并复习相关文献。结果患者,女,18岁,16年前接种卡介苗后反复咳嗽、咳痰、出现全身多发性包块,临床特征主要是血嗜酸性淋巴细胞增多、头颈部包块及淋巴结肿大和支气管扩张。颈部皮下肿物活检符合嗜酸性淋巴肉芽肿,对糖皮质激素治疗有效。结论 Kimura病属于少见病,合并支气管扩张是首例报道。
Objective To recognize the rare Kimura disease （KD）. Methods The clinical and pathological features of a KD patient with bronchiectasis admitted to our hospital on July 29,2008 was analyzed and related literature was reviewed. Results The patient was 18 years-old, female. Repeated cough, expectoration and systemic multiple mass appeared after bacillus Cahnette-Guerin Vaccine inoculation 16 years ago. The main clinical features included enlarged lymph nodes and mass in soft tissue of the head and neck region,eosinophilia and bronehiectasis. The biopsy of subcutaneous mass of neck was consistent with pathological features of eosinophylic lymphoid granuloma. The patient was sensitive to glucocortieoid therapy. Conclusions KD is a rare disorder. We present the first case of KD with bronehiectasis.
出处
《中华哮喘杂志（电子版）》
CAS
2010年第2期73-76,共4页
Chinese Journal of Asthma(Electronic Version)
