摘要
目的:探讨外周性原始神经外胚层肿瘤(pPNET)的影像学诊断价值,提高对本病的认识。方法:搜集我院经手术病理及免疫组化证实的pPNET 9例。CT检查6例,其中4例增强扫描;MRI平扫+增强检查3例;超声检查4例,分析pPNET的影像学表现特点。结果:发生于后胸壁2例,腰骶部、肩胛骨、鞍结节、鼻腔、颈部、右上臂及卵巢各1例。pPNET多表现为较大实体软组织肿块,成分混杂,血供相对较丰富,呈不均匀性强化;起源骨组织者以溶骨破坏为主,周围见明显软组织肿块;起源于胸壁pPNET常伴有胸膜侵犯及邻近肋骨骨质的破坏。结论:影像学检查能较好地显示pPNET大小、范围及其毗邻关系,对于青少年出现溶骨性破坏伴较大软组织肿块或软组织内见较大异质性肿块应考虑本病的可能,定性诊断仍依赖于病理学检查。
Objective：To investigate the imaging diagnostic value of primitive neuroectodermal tumors（pPNET） and to improve the recognition of it.Methods：9 cases of pPNET proved by clinic pathology and immunohistochemistry were collected in the study.6 cases had undergone CT scanning with contrast enhancement of 4 cases,3 cases had ungergone plain and enhanced MRI scanning,and 4 cases had undergone ultrasound examination.The imaging characteristics were retrospectively analyzed.Results：The locations of the tumors were posterior thoracic wall（n=2）,lumbosacral canal,scapula,sellar tuberculum,nasal cavity,neck,the right upper arm and ovary（n=1,corresprndingly）.The pPNET demonstrated large parenchymal soft tissue masses with different components,rather abundant blood supply and inhomogeneous enhancement.The tumors originated from bone tissue had irregular lytic one destruction with evident soft tissue masses.The tumors originated from thoracic wall were easy to invade pleural and destructe adjacent ribs.Conclusion：Imaging examination can better demonstrate the size,range and adjacent tissue relationship of pPNET.The possibility of pPNET diagnosis should be considered when it had lytic bone destruction with large soft tissue mass or inhomogeneous mass of soft tissue in youth,but its final diagnosis was still established by pathology examination.
出处
《医学影像学杂志》
2008年第7期720-723,共4页
Journal of Medical Imaging
