摘要
目的:通过分析心肌致密化不全患者的临床特点、诊断方法、治疗及预后,以提高临床诊治水平。方法:分析及随访2000年1月～2006年4月住院治疗的17例心肌致密化不全患者的临床资料、治疗及预后。结果:心肌致密化不全特征为海绵状心肌,多发生于左心室。临床表现主要为心力衰竭(纽约心功能分级Ⅱ～Ⅳ级者占88.2%)、心律失常及血栓形成(分别为88.2%与11.8%)。17例中14例为孤立性心肌致密化不全,3例合并其他心血管疾患。17例患者均行超声心动图及心脏磁共振检查,其中13例患者的超声心动图及心脏磁共振检查均明确诊断,另4例经心脏磁共振检查确诊。随访10例患者,3例行心脏移植手术,1例死亡。结论:心肌致密化不全临床表现各异,预后差。超声心动图检查是诊断主要方法,心脏磁共振检查有助于提高诊断水平。
Objective：To investigate the clinical features,treatment and prognosis of the ventricular noncompaction in 17 patients in order to improve diagnosis and treatment.
Methods：We analyzed clinical datum and followed up treatment and prognosis in 17 patients with the ventricular noncompaction from January 2000 to April 2006.
Results：The most common presentations were congestive heart failure （ 88.2% ）, arrhythmias （ 88. 2% ） and thrombosis （ 11.8% ）. The noncompaction of ventricular myocardium（NVM） was isolated, or occurred with other cardiovascular malformation. Echocardiography was a main method for diagnosis.
Conclusion： NVM has a long-term clinical course and diversity manifestations and usually has a poor prognosis. Echocardiography is a principal means of diagnosis. Magnetic resonance imaging can contribute to the diagnosis.
出处
《中国循环杂志》
CSCD
北大核心
2007年第2期114-117,共4页
Chinese Circulation Journal
关键词
心肌致密化不全
临床特点
诊断方法
Noncompaction of the ventricular myocardium
Clinical features
Methods of diagnosis
