摘要
目的探讨胎儿先天性肺囊腺瘤样畸形(CCAM)的 MRI 表现及其诊断价值。方法对9例超声诊断或怀疑为 CCAM 的胎儿在超声诊断后1～2 d 内进行 MR 检查并用单次激发快速自旋回波序列(SSFSE)行胎儿胸部轴面、矢状面和冠状面扫描,8例经引产后尸检及随访证实。结果8例引产胎儿中,MRI 诊断并尸检证实 CCAM 7例,隔离肺1例;1例 MRI 表现正常者,2周后复查B超无异常。其中 CCAM 发生于男性5例,女性2例;均单侧发病,位于右侧4例,左侧3例。大囊型CCAM 4例,MRI 表现为单侧肺内的长 T_2信号灶,比正常肺组织信号高,其中有单发或多发的囊状长T_2信号;微囊型3例,表现为一侧肺内长 T_2信号灶,其内未见明显囊状长 T_2信号。2例 CCAM 和1例隔离肺可显示病灶内血管流空征象,隔离肺的引流血管起源于降主动脉。结论 MRI 可清楚显示各型 CCAM 的病变部位、范围和轮廓。发现起源于主动脉的引流血管多提示隔离肺,有助于 CCAM 的鉴别诊断。
Objective To demonstrate the MRI manifestations of congenital cystic adenomatoid malformation（CCAM） and to evaluate the diagnostic value of MRI. Methods Thoracic axial, sagittal and coronal plane scanning were performed with SSFSE in 9 fetuses diagnosed or suspected of CCAM by ultrasound（US） within 1-2 days after US examination. The diagnosis was confirmed by postnatal autopsy or follow-up. Results In nine fetuses, seven cases of CCAM were diagnosed with MRI and confirmed by autopsy, one case was congenital pulmonary sequestration, one was normal on MRI and two weeks late US. In seven cases of CCAM （5 males and 2 females）, four cases were in the right side,three in the left. Four cases of macrocystic type CCAM showed single or multiple cystic long T2 signal in the unilateral lung, three cases of microcystic type CCAM presented long T2 signal without cyst. Vessels with flow void phenomenon were found in 2 cases of CCAM and 1 case of pulmonary sequestration. Conclusion MRI can clearly show the location, range and contour of CCAM. The vessel originated from the aorta is suggestive of pulmonary sequestration.
出处
《中华放射学杂志》
CAS
CSCD
北大核心
2007年第5期490-492,共3页
Chinese Journal of Radiology
关键词
胎儿
囊腺瘤样畸形
肺
先天性
磁共振成像
Fetus
Cystic adenomatoid malformation of lung, congenital
Magnebc resonance imaging
