摘要
目的探讨儿童Klippel-Feil综合征的影像学诊断及其影像学检查技术的应用价值。方法Klippel-Feil综合征患儿6例,男4例,女2例,年龄4-12岁,平均6岁。6例患儿均行X线平片及螺旋CT检查。结果6例患儿均显示两节或多节颈椎椎体融合畸形,同时合并脊柱侧弯3例、椎体畸形2例、颈椎椎板闭合不全2例、寰枢关节旋转错位1例。结论儿童Klippel-Feil综合征典型的临床表现为短颈、后发际低及颈椎活动受限,结合颈椎融合畸形等典型的影像学表现,可作出明确诊断。
Objective：To evaluate the radiologic diagnosis of pediatric Klippel-Feil syndrome and the applied value of every radiography about Klippel-Feil syndrome. Methods：Six cases,4 males and 2 females, were examined. The ages were 4 to 12,with an average of 6. All cases underwent X-ray and spiral CT examination before therapy. Results：X-ray and CT of the cervical spines showed fusions at one level or several levels in all 6 cases;at the same time complicated scoliosis in 3 cases,vertebral body malformation in 2 cases, spina bifida in 2 cases, and atlantoaxial rotated dystopia in 1 case. Conclusion： Definite diagnosis of pediatric Klippel-Feil syndrome can be made according to the classical clinical symptoms including short neck,low posterior hairline,and reduced neck movement associated with typical radiological manifestations.
出处
《放射学实践》
2007年第4期345-347,共3页
Radiologic Practice
