摘要
目的总结双肾血管平滑肌脂肪瘤(RAML)伴结节性硬化症(TSC)的发病特点,以提高该病的诊治水平.方法回顾性分析4例双RAML伴TSC患者的临床资料.结果 4例患者经B超、CT检查诊断.1例因左肾肿瘤出血行肾切除,1例因右肾肿瘤巨大行肾切除.另2例患者因肿瘤小且症状轻微行保守治疗,随访12～48个月,肿瘤大小无变化,无症状复发.结论 B超、CT检查结合临床表现是诊断RAML伴TSC的重要手段.治疗方案应根据双肾肿瘤的大小、分布、发展情况及症状决定.手术时应注意保留正常肾组织,保护肾功能.
Objective To summarize the clinical features of bilateral multiple renal angiomyolipomas associated with tuberous sclerosis and improve the diagnosis and treatment. Methods Clinical data of 4 cases of bilateral multiple renal angiomyolipomas associated with tuberous sclerosis were analyzed retrospectively, Results The diagnosis of renal angiomyolipomas associated with tuberous sclerosis in 4 cases was confirmed by CT scanning. One patient with hemorrhage in renal angiomyolipomas was subjected to nephrectomy, and one to right nephrectomy for the large lesions. Regular monitoring of two patients withconservative therapy was adopted for mild symptomatic small renal lesion. Fellow - up ranged 12 to 48 months. None had recurrent symptoms and no significant growth of renal lesion was observed. Conclusion Ultrasonography and CT are important methods to diagnose and the choice of treatment is based on tumor size, distribution pattern, progression and associated symptoms. Attention should be paid to reserve the renal tissue as much as possible and renal function should be protected properly.
出处
《临床外科杂志》
2005年第11期714-715,共2页
Journal of Clinical Surgery
