摘要
Caroli病为先天性肝胆管扩张症,常伴肝外胆管扩张。本文报告1983~1992年31例;根据影象诊断(B超31例,CT9例,MRI2例,ERCP24例,PTC7例等)及手术发现,本组属双侧型24例,单侧型7例,合并肝外胆管扩张29例,2例癌变。全组手术25例,术后死亡1例,余24例随访,疗效优良者18例(75%),差6例(25%)。文中讨论了Caroli病的影象诊断;提出了本病的治疗原则;对不同类型手术方式进行了讨论;本病易于癌变,彻底切除肝内囊肿及通畅引流,以从根本上消除癌变基础。
aroli disease refers to the condition of congenital intrahepatic bjle
duct dilatation, usuallyaccompanied with extrahepatic bile duct dilatation. This article reported
31 cases attended from 1983 to1992. lmaging diagnostic procedures(B-Mode Ultrasonography
in 31 cases,CT in 9,MRI in 2, ERCPin 24,and PTC in 7)and operative findings indicatived that,
in this group there were 24 eases ofbilateral type and 7 cases of unilateral type; 29 cases had
concurrent extrahepatic bile duct dilatation,whereas 2 demonstrated malignant neoplasms.
Twenty-five cases in this group underwent surgery andl died after operation. The remaining 24
cases were followed-up. Excellent or goed long-termresults were seen in 18 cases(75%) , while
the other 6 cases were unsatisfactory (25 % ).In this paper, the imaging diagncais of Caroli
disease was discussed ,some principles of treatment wereadvocated ,and different types of
surgical prcoedures for the disease were evaluated. Caroli disease isprone to malignant
transformation ,so it is essential to make radical resection of the dilatated bile ductand form a
fluent draining conduit in order to eleminate the basis for malignant transformation.
出处
《中国普通外科杂志》
CAS
CSCD
1994年第1期1-4,共4页
China Journal of General Surgery
关键词
胆管囊性扩张
肝内
外科手术
Caroli disease
lmaging diagnosis
Intrahepatic bile duct dilatation.