摘要
目的探讨家族性巨颌症临床特点及治疗。方法对7例患者的临床资料进行回顾性分析。结果临床表现为广泛性、无痛性和对称性的上下颌骨膨隆,下颌骨(7/7)多于上颌骨(4/7)。3例有家族史。X线表现为多房囊性阴影。4例术前得到正确诊断。5例采用保守的手术治疗。结论家族性巨颌症应与巨细胞肉芽肿及骨巨细胞瘤相鉴别。由于该病青春期后有自愈性,较轻的患者无需手术,较严重的患者保守的手术治疗效果理想。
Objective To study the clinical features and treatment of cherubism Methods The clinical data of 7 cases were analyzed retrospectively. Results The patients presented with progressive, painless, symmetrical expansion of the maxilla and mandible. 3 cases had the positive family history. The lesions showed the appearances of bilateral multilocular radiolucent area on radiography. 4 cases had been confirmed diagnosis before operations. 5 cases underwent the conservative operations. Conclusion cherubism should be differentiatied with giant cell granulomas and giant cell tumor of bone. The majority patients with cherubism can recover by themselves after puberty. The therapy effect of conservative operation in serious cases is satisfied.
出处
《罕少疾病杂志》
2004年第5期4-6,共3页
Journal of Rare and Uncommon Diseases
关键词
巨颌症
巨细胞肉芽肿
诊断
治疗
cherubism
giant cell granulomas
diagnosis
treatment
