PURPOSE: To describe the treatment of juxtapapillary capillary angioma by pars plana vitrectomy (PPV) and tumor excision. DESIGN: Interventional case report. METHODS:A6-year-old girl with symptomatic juxtapapillary ca...PURPOSE: To describe the treatment of juxtapapillary capillary angioma by pars plana vitrectomy (PPV) and tumor excision. DESIGN: Interventional case report. METHODS:A6-year-old girl with symptomatic juxtapapillary capillary retinal angioma with associated epiretinal membrane (ERM) underwent PPV and extraction of the tumor and ERM. A clinical and molecular genetic workup for the presence of von Hippel-Lindau disease (VHL) was performed. RESULTS: A favorable functional result without tumor recurrence was achieved. Capillary retinal angioma was confirmed by histology of the surgical specimen,and familial VHL was revealed. CONCLUSIONS: PPV and extraction of the tumor is applicable in juxtapapillary capillary retinal angioma with associated ERM. A workup for the presence of VHL is pertinent in patients presenting with this tumor entity.展开更多
文摘PURPOSE: To describe the treatment of juxtapapillary capillary angioma by pars plana vitrectomy (PPV) and tumor excision. DESIGN: Interventional case report. METHODS:A6-year-old girl with symptomatic juxtapapillary capillary retinal angioma with associated epiretinal membrane (ERM) underwent PPV and extraction of the tumor and ERM. A clinical and molecular genetic workup for the presence of von Hippel-Lindau disease (VHL) was performed. RESULTS: A favorable functional result without tumor recurrence was achieved. Capillary retinal angioma was confirmed by histology of the surgical specimen,and familial VHL was revealed. CONCLUSIONS: PPV and extraction of the tumor is applicable in juxtapapillary capillary retinal angioma with associated ERM. A workup for the presence of VHL is pertinent in patients presenting with this tumor entity.
