Summary: Poland syndrome is a rare congenital anomaly characterized by the partial or complete absence of the pectoralis major muscle and a wide spectrum of thoracic anomalies, predominantly on the ipsilateral side. T...Summary: Poland syndrome is a rare congenital anomaly characterized by the partial or complete absence of the pectoralis major muscle and a wide spectrum of thoracic anomalies, predominantly on the ipsilateral side. These anomalies include hypoplasia or aplasia of the breast and its components, hypotrophy of subcutaneous fat, and absence of axillary hair, as well as hand deformities that can range from syndactyly to ectrodactyly. The aim of this study was to gather information about patients diagnosed with Poland syndrome at the Central South High Specialty Hospital of Petróleos Mexicanos over a period of 10 years and to identify their reconstructive algorithm. Materials and Methods: A retrospective, observational, and descriptive study was conducted to identify the population diagnosed with Poland syndrome at the “Central South High Specialty Hospital of Petróleos Mexicanos” during the period from 2013 to 2023. Results: The database of patients with Poland syndrome from 2013 to 2023 was analyzed, identifying a total of 8 patients with this diagnosis. Of these, 7 were women (90%) and 1 was a man (10%). The left side was more frequently affected (80%) compared to the right side (20%). The average reconstructive process required two surgical stages, mainly consisting of breast expander reconstruction (first stage) and replacement of the expander with an implant (second stage). Conclusions: Despite being a rare congenital condition, the volume of patients treated at the Central South High Specialty Hospital allows for improved diagnosis and contributes to their reconstructive process. The lack of diagnosis in the male population is notable, likely due to the absence of adequate screening.展开更多
目的探讨加速康复外科(enhanced recovery after surgery,ERAS)应用于Poland综合征患儿手指矫形围手术期中的临床效果。方法将自2016年6月至2018年6月收治的35例Poland综合征患儿作为对照组,行传统围手术期管理模式;自2018年7月至2020年...目的探讨加速康复外科(enhanced recovery after surgery,ERAS)应用于Poland综合征患儿手指矫形围手术期中的临床效果。方法将自2016年6月至2018年6月收治的35例Poland综合征患儿作为对照组,行传统围手术期管理模式;自2018年7月至2020年6月收治的35例Poland综合征患儿作为研究组,行加速康复外科管理模式。手术均一次性行2~5指并指分离术,统计两组患儿手术时间、麻醉时间、术后各时间段疼痛情况、术后不良反应发生情况、住院时间、住院费用以及家属满意度。结果研究组术后2、6、12 h的改良面部表情法(FLACC)疼痛评分明显低于对照组,且术后不良反应发生率低(P<0.05)。研究组相对于对照组的住院时间短、住院费用低、家属满意度高(P<0.05)。结论ERAS应用于Poland综合征患儿手指矫形围手术期管理,能降低围手术期疼痛指数,在减少术后不良反应发生的同时加速机体康复,从而达到缩短住院时间的目的,值得临床推广。展开更多
文摘Summary: Poland syndrome is a rare congenital anomaly characterized by the partial or complete absence of the pectoralis major muscle and a wide spectrum of thoracic anomalies, predominantly on the ipsilateral side. These anomalies include hypoplasia or aplasia of the breast and its components, hypotrophy of subcutaneous fat, and absence of axillary hair, as well as hand deformities that can range from syndactyly to ectrodactyly. The aim of this study was to gather information about patients diagnosed with Poland syndrome at the Central South High Specialty Hospital of Petróleos Mexicanos over a period of 10 years and to identify their reconstructive algorithm. Materials and Methods: A retrospective, observational, and descriptive study was conducted to identify the population diagnosed with Poland syndrome at the “Central South High Specialty Hospital of Petróleos Mexicanos” during the period from 2013 to 2023. Results: The database of patients with Poland syndrome from 2013 to 2023 was analyzed, identifying a total of 8 patients with this diagnosis. Of these, 7 were women (90%) and 1 was a man (10%). The left side was more frequently affected (80%) compared to the right side (20%). The average reconstructive process required two surgical stages, mainly consisting of breast expander reconstruction (first stage) and replacement of the expander with an implant (second stage). Conclusions: Despite being a rare congenital condition, the volume of patients treated at the Central South High Specialty Hospital allows for improved diagnosis and contributes to their reconstructive process. The lack of diagnosis in the male population is notable, likely due to the absence of adequate screening.
文摘目的探讨加速康复外科(enhanced recovery after surgery,ERAS)应用于Poland综合征患儿手指矫形围手术期中的临床效果。方法将自2016年6月至2018年6月收治的35例Poland综合征患儿作为对照组,行传统围手术期管理模式;自2018年7月至2020年6月收治的35例Poland综合征患儿作为研究组,行加速康复外科管理模式。手术均一次性行2~5指并指分离术,统计两组患儿手术时间、麻醉时间、术后各时间段疼痛情况、术后不良反应发生情况、住院时间、住院费用以及家属满意度。结果研究组术后2、6、12 h的改良面部表情法(FLACC)疼痛评分明显低于对照组,且术后不良反应发生率低(P<0.05)。研究组相对于对照组的住院时间短、住院费用低、家属满意度高(P<0.05)。结论ERAS应用于Poland综合征患儿手指矫形围手术期管理,能降低围手术期疼痛指数,在减少术后不良反应发生的同时加速机体康复,从而达到缩短住院时间的目的,值得临床推广。
基金北京市“十百千”卫生人才“十层次”基金，首都临床特色项目基金，"Ten Level" Fund of "Ten Hundred Thousand" Health Talent Fund of Beijing，Clinical Characteristic Project Fund of Capital
