Melorheostosis, also known as Leri disease or flowing periosteal hyperostosis, is a rare, non-hereditary, benign, skle-rosing bone dysplasia which radiologically characterized by the appearance of “melting wax flowin...Melorheostosis, also known as Leri disease or flowing periosteal hyperostosis, is a rare, non-hereditary, benign, skle-rosing bone dysplasia which radiologically characterized by the appearance of “melting wax flowing down a candle”. We report on a 43-year-old woman with melorheostosis who had pain in the upper limp for 10 years, limitation of joint movement and a deformity in the left third finger. Radiographies and bone scintigraphy were evaluated. All lesions of melorheostosis in radiography were seen in bone scintigraphy. More than half of increased uptakes on bone scintigra-phy are due to degenerative process.展开更多
Melorheostosis is a rare form of sclerosing bone dysplasia that involves mainly the long bone of the limbs. However, the involvement of more than one long bone, either involving ipsilaterally or contralaterally, is ex...Melorheostosis is a rare form of sclerosing bone dysplasia that involves mainly the long bone of the limbs. However, the involvement of more than one long bone, either involving ipsilaterally or contralaterally, is extremely rare. The aetiology still remains unknown despite approximately 400 cases have been reported in the literature up to date. Diagnosis is mainly by conventional radiographic imaging such as plain X-ray, in which the typical melting wax dripping down a candle appearance is seen. The main treatment options are conservative management involving mainly analgesias, physiotherapy, braces, and possible nerve block and symphathectomies if indicated. The aim of this case report is to discuss the approach to a case of melorheostosis involving two long bones of the ipsilateral lower limb (polyostotic) that presented to us in our centre. Appropriate investigations and treatment modalities must be tailored according to the patient’s complaints in order to achieve satisfactory treatment outcomes. With adequate analgesia complimenting with appropriate physiotherapy and rehabilitation, our patient’s symptoms improved dramatically.展开更多
文摘Melorheostosis, also known as Leri disease or flowing periosteal hyperostosis, is a rare, non-hereditary, benign, skle-rosing bone dysplasia which radiologically characterized by the appearance of “melting wax flowing down a candle”. We report on a 43-year-old woman with melorheostosis who had pain in the upper limp for 10 years, limitation of joint movement and a deformity in the left third finger. Radiographies and bone scintigraphy were evaluated. All lesions of melorheostosis in radiography were seen in bone scintigraphy. More than half of increased uptakes on bone scintigra-phy are due to degenerative process.
文摘Melorheostosis is a rare form of sclerosing bone dysplasia that involves mainly the long bone of the limbs. However, the involvement of more than one long bone, either involving ipsilaterally or contralaterally, is extremely rare. The aetiology still remains unknown despite approximately 400 cases have been reported in the literature up to date. Diagnosis is mainly by conventional radiographic imaging such as plain X-ray, in which the typical melting wax dripping down a candle appearance is seen. The main treatment options are conservative management involving mainly analgesias, physiotherapy, braces, and possible nerve block and symphathectomies if indicated. The aim of this case report is to discuss the approach to a case of melorheostosis involving two long bones of the ipsilateral lower limb (polyostotic) that presented to us in our centre. Appropriate investigations and treatment modalities must be tailored according to the patient’s complaints in order to achieve satisfactory treatment outcomes. With adequate analgesia complimenting with appropriate physiotherapy and rehabilitation, our patient’s symptoms improved dramatically.
文摘蜡泪样骨病（ Melorheostosis ）是临床上一种罕见的原因不明的骨骼发育障碍性疾病。常常侵犯一侧肢体，且下肢多见，增生的骨质从上而下沿骨干一侧向下流注，酷似蜡烛表面的烛泪，故名蜡泪样骨病，又称单肢型骨硬化、流动性骨质硬化症、蜡油样骨病、肢骨纹状肥大症等[1-2]。本病可根据 X 线特有的改变及病理学检查确诊，国内外均罕见，唐山市第二医院骨病科于2016年收治1例，现报道如下。
