目的:探讨产前超声在胎儿先天性肺囊腺瘤畸形(congenital cystic adenomatiod malformation of the lung,CCAM)诊断中的价值及临床意义。方法:对产前超声疑诊为CCAM的30例胎儿的声像图特征进行回顾性分析,并随访其临床结果。结果:超声...目的:探讨产前超声在胎儿先天性肺囊腺瘤畸形(congenital cystic adenomatiod malformation of the lung,CCAM)诊断中的价值及临床意义。方法:对产前超声疑诊为CCAM的30例胎儿的声像图特征进行回顾性分析,并随访其临床结果。结果:超声疑诊的30例CCAM胎儿中,单侧病变为28例,双侧病变为2例;CCAMⅠ型6例,Ⅱ型6例,Ⅲ型18例;有8例孕妇选择引产,余22例活产;所有活产病例产后随访至12个月,婴儿均无异常。结论:超声检查是发现胎儿肺内CCAM病灶的重要方法,在发现该病灶后,可应用超声观察病灶变化,单纯CCAM且不合并胎儿水肿的患儿出生后预后较好。展开更多
Objective To investigate the ultrasonic detection probability, type, prenatal diagnosis, and outcome of congenital cystic adenomatoid malformation of lung （CCAM）. Methods In this retrospective study, all 12 cases wh...Objective To investigate the ultrasonic detection probability, type, prenatal diagnosis, and outcome of congenital cystic adenomatoid malformation of lung （CCAM）. Methods In this retrospective study, all 12 cases which were diagnosed with suspected prenatal CC,4M over the period in the hospital were analyzed. Information on diagnosis time, types and progression of the lesions during pregnancy, the additional abnormalities, and the outcome of pregnancies were recorded.Results The positive rate of ultrasonic detection of CCAM was about 1.01‰ （1/11 124） before 28 gestation weeks. There were 1 case of type Ⅰ （8%）, 2 cases of type Ⅱ （17%） and 9 cases of type Ⅲ （75%）. Nine pregnancies were terminated and 2 cases were confirmed by pathology. Three neonates were alive and without any symptom now. Conclusions Type Ⅲ is the major type. Ultrasound examination during 20-28 weeks and following up, prenatal consultation, chromosome examination offetus, delivery with a pediatrician standing by, and all suspected neonates being investigated are recommended.展开更多
儿童先天性肺囊性腺瘤样畸形(congenital cystic adenomatoid malformation of the lung,CCAM)是临床少见肺部疾病,是肺组织胚胎发育异常所形成的畸形,其病理形态与其他类型的肺囊肿截然不同.现对CCAM的主要发病机制、临床表现、诊断与...儿童先天性肺囊性腺瘤样畸形(congenital cystic adenomatoid malformation of the lung,CCAM)是临床少见肺部疾病,是肺组织胚胎发育异常所形成的畸形,其病理形态与其他类型的肺囊肿截然不同.现对CCAM的主要发病机制、临床表现、诊断与鉴别诊断、治疗措施进行综述.展开更多
文摘目的:探讨产前超声在胎儿先天性肺囊腺瘤畸形(congenital cystic adenomatiod malformation of the lung,CCAM)诊断中的价值及临床意义。方法:对产前超声疑诊为CCAM的30例胎儿的声像图特征进行回顾性分析,并随访其临床结果。结果:超声疑诊的30例CCAM胎儿中,单侧病变为28例,双侧病变为2例;CCAMⅠ型6例,Ⅱ型6例,Ⅲ型18例;有8例孕妇选择引产,余22例活产;所有活产病例产后随访至12个月,婴儿均无异常。结论:超声检查是发现胎儿肺内CCAM病灶的重要方法,在发现该病灶后,可应用超声观察病灶变化,单纯CCAM且不合并胎儿水肿的患儿出生后预后较好。
基金This study is supported by 2004-2006 important clinic studies of medical institutions belonging to the Health Care Ministry of China
文摘Objective To investigate the ultrasonic detection probability, type, prenatal diagnosis, and outcome of congenital cystic adenomatoid malformation of lung （CCAM）. Methods In this retrospective study, all 12 cases which were diagnosed with suspected prenatal CC,4M over the period in the hospital were analyzed. Information on diagnosis time, types and progression of the lesions during pregnancy, the additional abnormalities, and the outcome of pregnancies were recorded.Results The positive rate of ultrasonic detection of CCAM was about 1.01‰ （1/11 124） before 28 gestation weeks. There were 1 case of type Ⅰ （8%）, 2 cases of type Ⅱ （17%） and 9 cases of type Ⅲ （75%）. Nine pregnancies were terminated and 2 cases were confirmed by pathology. Three neonates were alive and without any symptom now. Conclusions Type Ⅲ is the major type. Ultrasound examination during 20-28 weeks and following up, prenatal consultation, chromosome examination offetus, delivery with a pediatrician standing by, and all suspected neonates being investigated are recommended.
基金国家自然科学基金(81371449)%The National Natural Science Fund of China(81371449)
文摘儿童先天性肺囊性腺瘤样畸形(congenital cystic adenomatoid malformation of the lung,CCAM)是临床少见肺部疾病,是肺组织胚胎发育异常所形成的畸形,其病理形态与其他类型的肺囊肿截然不同.现对CCAM的主要发病机制、临床表现、诊断与鉴别诊断、治疗措施进行综述.
