Congenital rubella syndrome is characterized by the triad of deafness, cataract and cardiovascular mafformations. The great majority of the cases in the literature have been usually diagnosed in infancy and childhood ...Congenital rubella syndrome is characterized by the triad of deafness, cataract and cardiovascular mafformations. The great majority of the cases in the literature have been usually diagnosed in infancy and childhood because of various defects at birth. However, we report a rare case of suspected congenital rubella syndrome in an adult with unilateral pulmonary artery stenosis and late-onset cataract.展开更多
Extrinsic compression of the pulmonary arteries by mediastinal masses, while rare, is the most common cause of non-congenital peripheral pulmonary artery stenosis. Granulocytic myeloid sarcomas are an extramedullary m...Extrinsic compression of the pulmonary arteries by mediastinal masses, while rare, is the most common cause of non-congenital peripheral pulmonary artery stenosis. Granulocytic myeloid sarcomas are an extramedullary manifestation of acute myeloid leukemia, with a wide variability in their presentation. They can present either de novo as soft tissue masses or in conjunction with acute myeloid leukemia. Myeloid sarcomas are uncommon and their prognosis is generally considered poor when present in patients with acute myeloid leukemia (AML). We present a case of a granulocytic myeloid sarcoma causing pulmonary artery stenosis and right ventricular failure. This case represents a unique cause of pulmonary arterial stenosis.展开更多
This is a very unusual case with unexpected findings. In spite of sophisticated investigation tests such as MRI and pul?monary angiogram, it may be very difficult to identify the nature of pulmonary artery stenosis or...This is a very unusual case with unexpected findings. In spite of sophisticated investigation tests such as MRI and pul?monary angiogram, it may be very difficult to identify the nature of pulmonary artery stenosis or occlusion.展开更多
文摘Congenital rubella syndrome is characterized by the triad of deafness, cataract and cardiovascular mafformations. The great majority of the cases in the literature have been usually diagnosed in infancy and childhood because of various defects at birth. However, we report a rare case of suspected congenital rubella syndrome in an adult with unilateral pulmonary artery stenosis and late-onset cataract.
文摘Extrinsic compression of the pulmonary arteries by mediastinal masses, while rare, is the most common cause of non-congenital peripheral pulmonary artery stenosis. Granulocytic myeloid sarcomas are an extramedullary manifestation of acute myeloid leukemia, with a wide variability in their presentation. They can present either de novo as soft tissue masses or in conjunction with acute myeloid leukemia. Myeloid sarcomas are uncommon and their prognosis is generally considered poor when present in patients with acute myeloid leukemia (AML). We present a case of a granulocytic myeloid sarcoma causing pulmonary artery stenosis and right ventricular failure. This case represents a unique cause of pulmonary arterial stenosis.
文摘This is a very unusual case with unexpected findings. In spite of sophisticated investigation tests such as MRI and pul?monary angiogram, it may be very difficult to identify the nature of pulmonary artery stenosis or occlusion.
